Successfully Anesthetic Management in a Rare Syndrome, Noonan Syndrome: Case Report-Juniper Publishers
Juniper Publishers - Journal of Anesthesia Abstract Noonan's Syndrome (NS) is a multisystem congenital disorder and characterized by fascial and pysical fatures along with congenital heart disease. In these patients, fascial features include short webbed neck, micrognathia, limited mouth opening and high arched palate can be a big problem for the tracheal intubation. Most commonly associated cardiac anomaly is pulmonary stenosis (>50% of cases). In these patients anesthetic management is important because of difficult airway and severe cardiac abnormalities. Here, we have reported the preoperative evaluation and anaesthetic management of a child with NS complicated by pulmonary stenosis and laringomalasia. Keywords: Congenital heart surgery; Noonan's syndrome; Difficult intubation; Pulmonary stenosis Abbreviation: NS: Noonan's Syndrome; PS: Pulmonary Stenosis; HOCM: Hypertrophic Obstructive Cardiomyopathy; ASD: Atrial Septal Defect; RVOTR: Right Ve...